Childhood-onset primary Sjogren's syndrome in a tertiary center in China: clinical features and outcome.

ABSTRACT:

Objectives

To characterize the clinical features and outcomes of childhood-onset primary Sjögren's syndrome (pSS).

Methods

Patients less than 18 years old who were diagnosed with pSS by paediatric rheumatologists were included, and all patients were applied the 2002 American-European Consensus Group (ACEG) criteria, the 2016 American College of Rheumatology/European League Against Rheumatism (ACR/EULAR) criteria for pSS, or the 1999 proposed juvenile pSS criteria. The electronic medical records of patients with pSS from 2013 to 2020 were collected and analysed.

Results

Thirty-nine patients were included. Of them, 27 (69.2%), 38 (97.4%) and 35 (89.7%) patients fulfilled the AECG criteria, ACR/EULAR criteria and proposed juvenile pSS criteria, respectively. The female:m

SUBMITTER: Gong Y 

PROVIDER: S-EPMC9881323 | biostudies-literature | 2023 Jan

REPOSITORIES: biostudies-literature