Lost in transition: a case report of very late palliation of a double outlet right ventricle.

ABSTRACT:

Background

Children with congenital heart disease remain at risk of being lost to follow-up. They may present at a later stage with complications related to underlying condition that usually require in-depth phenotyping for optimal management. We describe an unusual case of a double outlet right ventricle (DORV) who presented three decades after initial intervention.

Case summary

A 32-year-old female sought attention for worsening breathlessness. Available data suggested that she had double outlet right ventricle (DORV) and underwent pulmonary artery (PA) banding in infancy. On examination, she was frail, clubbed and cyanosed with oxygen saturation reduced to 75% at rest. Blood tests demonstrated elevated haemoglobin (208 g/L) and thrombocytopenia (70 *10⁹/L). Ech

SUBMITTER: Ahmed R 

PROVIDER: S-EPMC9883723 | biostudies-literature | 2023 Jan

REPOSITORIES: biostudies-literature