Alveolar capillary dysplasia with misalignment of pulmonary veins in a premature newborn: the role of lung ultrasound.

ABSTRACT:

Background

Alveolar capillary dysplasia with misalignment of pulmonary veins (ACD/MPV) is a lethal neonatal lung disorder characterized by the decrease of the alveolar units, abnormalities in the air-blood barrier of the lung, and impaired gas exchange. Typically, it affects a full-term newborn; the symptoms usually start within a few hours after birth, resulting in severe respiratory distress and pulmonary hypertension. In most of the cases, this disorder is refractory to conventional pulmonary support.

Case presentation

We report a case of a newborn male of 29 weeks gestational age, with birth weight of 850 g and intrauterine growth restriction. Severe respiratory distress appeared a few minutes after birth; non-invasive ventilatory support was provided in the delivery roo

SUBMITTER: Atun ML 

PROVIDER: S-EPMC9922097 | biostudies-literature | 2023 Feb

REPOSITORIES: biostudies-literature