Pediatric bronchial Dieulafoy's disease with bronchial artery embolization: two case reports.

ABSTRACT:

Background

Bronchial Dieulafoy's disease (BDD) is a vascular malformation characterized by the presence of a dysplastic artery in the bronchial submucosa. It is very rare in children but potentially fatal due to life-threatening hemoptysis.

Case description

An 8-year-old boy and a 6-year-old girl were referred to our hospital with recurrent moderate to massive hemoptysis. Intraluminal protrusions with a tendency to bleed were found by bronchoscopy in both patients. Computed tomography angiography (CTA) revealed an abnormal bronchial artery in one patient and a small intraluminal nodule with contrast enhancement in the other. An enlarged bronchial artery and bronchial-to-pulmonary fistulae corresponding to the lesion site were detected by bronchial arteriography in both patie

SUBMITTER: Lai L 

PROVIDER: S-EPMC9926130 | biostudies-literature | 2023 Jan

REPOSITORIES: biostudies-literature