Criteria for progressive fibrotic hypersensitivity pneumonitis in a Portuguese patient cohort.

ABSTRACT:

Background

Hypersensitivity pneumonitis (HP) is a syndrome caused by sensitisation to inhaled antigens that leads to an abnormal immune response in the airways and lung parenchyma. Some patients previously diagnosed with certain types of fibrotic interstitial lung diseases (f-ILDs), including fibrotic HP (f-HP), are susceptible to develop a progressive fibrosing phenotype (PF-ILD), despite initial state-of-the-art management.

Objectives

To characterise a cohort of patients with a multidisciplinary diagnosis (MTD) of chronic f-HP, who were followed up in an ILD outpatient clinic of a hospital in Portugal, and to assess the prevalence of PF-ILD criteria in these patients.

Methods

Data were collected from all patients with a definite or provisional diagnosis of f-HP afte

SUBMITTER: Seixas E 

PROVIDER: S-EPMC9929648 | biostudies-literature | 2022

REPOSITORIES: biostudies-literature