Resting and total energy expenditure of patients with long-chain fatty acid oxidation disorders (LC-FAODs).

ABSTRACT: The basis of medical nutrition therapy for patients with LC-FAODs is to provide adequate energy to maintain anabolism and prevent catabolism. In practice, energy needs are estimated based on formulas derived from normal populations but it is unknown if energy expenditure among patients with LC-FAODs is similar to the normal population. We measured resting energy expenditure (REE), total energy expenditure (TEE) and body composition in 31 subjects with LC-FAODs ranging in age from 7 to 64 years. Measured REE was lower than estimated REE by various prediction equations and measured TEE was lower than estimated TEE. It is possible that the lower energy expenditure based on prediction formulas from the normal population is due to differences in body composition; we compared body composition to

SUBMITTER: DeLany JP 

PROVIDER: S-EPMC9992335 | biostudies-literature | 2023 Mar

REPOSITORIES: biostudies-literature