Congenital bile duct cyst (BDC) is a more indolent disease in children compared to adults, except for Todani type IV-A BDC: results of the European multicenter study of the French Surgical Association.

ABSTRACT:

Aim

To compare clinical presentation, operative management and short- and long-term outcomes of congenital bile duct cysts (BDC) in adults with children.

Methods

Retrospective multi-institutional Association Francaise de Chirurgie study of Todani types I+IVB and IVA BDC.

Results

During the 37-year period to 2011, 33 centers included 314 patients (98 children; 216 adults). The adult population included more high-risk patients, with more active, more frequent prior treatment (47.7% vs 11.2%; p < 0.0001), more complicated presentation (50.5% vs 35.7%; p = 0.015), more synchronous biliary cancer (11.6% vs 0%; p = 0.0118) and more major surgery (23.6% vs 2%; p < 0.0001), but this latter feature was only true for type I+IVB BDC. Compared to children, the postoperative morbi

SUBMITTER: Ouaissi M 

PROVIDER: S-EPMC4913142 | biostudies-literature | 2016 Jun

REPOSITORIES: biostudies-literature