Generalised hypomineralisation of enamel in oculodentodigital dysplasia: comprehensive dental management of a case.

ABSTRACT: Oculodentodigital dysplasia (ODDD) is a rare congenital disorder characterised by developmental abnormalities of the eye, dentition and digits of the hands and feet, with neurological symptoms reported in 30% of individuals. Dental anomalies associated with ODDD include enamel hypoplasia and subsequent caries, microdontia, missing teeth, amelogenesis imperfecta, pulp stones and delayed tooth development. Here, we describe the comprehensive dental management of a 3-year-old girl who presented with rapid deterioration of the primary dentition due to generalised enamel hypomineralisation. Conservative, comprehensive restorative management was performed under general anaesthesia. Within 6 months, further breakdown of the remaining unrestored enamel was noted. This case documents the challenges

SUBMITTER: Jensen ED 

PROVIDER: S-EPMC7802714 | biostudies-literature | 2021 Jan

REPOSITORIES: biostudies-literature